由于新陳代謝較慢，小胖患者只能消耗同齡人所能消耗的60%的千焦熱量。這也只能是保持體重，如果需要減肥，那攝入的熱量則應(yīng)該更少。

營(yíng)養(yǎng)起著至關(guān)重要的作用，以確保每一口都有價(jià)值。此外，小胖患者處理碳水化合物的效率較低，攝入碳水化合物后更容易發(fā)胖。

小胖患者攝入精制碳水化合物后，大腦中的獎(jiǎng)勵(lì)機(jī)制更加明顯，這使他們幾乎上癮。一項(xiàng)為期五年的研究得出結(jié)論，低碳水化合物、適量蛋白質(zhì)和優(yōu)質(zhì)脂肪的飲食更有益。

纖維也是飲食結(jié)構(gòu)中極為重要的部分，高復(fù)合碳水化合物也主要來(lái)源于蔬菜。研究還表明，正確的飲食可以提高能量水平、學(xué)習(xí)能力、語(yǔ)言能力、情緒和腸道活動(dòng)能力。

由于很難定期獲得針對(duì)這些特殊需求的專業(yè)營(yíng)養(yǎng)建議，父母往往被迫承擔(dān)這一角色。許多父母花費(fèi)無(wú)數(shù)的時(shí)間研究，然后準(zhǔn)備飯菜。飲食的比例和份額要時(shí)刻檢查和控制。

因此，當(dāng)家人和朋友說(shuō)來(lái)吧，多一個(gè)沒(méi)什么，或你確定他吃飽了嗎？或他是一個(gè)成長(zhǎng)中的男孩，需要更多的碳水化合物時(shí)，這是非常令人沮喪的。大多數(shù)小胖的飲食是不允許有額外的東西的。

英文原文

PWS AND NUTRITION

With a slower metabolism people with PWS can only consume 60% of the kilojoules that someone else of the same age can.? This is to maintain weight – less if weight loss if required.

Nutrition plays a vital role, to make sure that every mouthful counts.

Additionally, people with PWS are less effective at processing carbohydrates and put on weight much more easily when they are consumed.? The reward mechanism in the brain is more pronounced with the consumption of refined carbohydrates for people with PWS, making them almost addictive.

?

A five-year research study concluded that a diet lower in carbohydrates, moderate in protein and increased quality fats is more beneficial.? Fibre is an extremely important component of this mix also.? The carbohydrates need to be complex and mostly derived from vegetables.

Research also suggests a diet rich in the right foods can improve energy levels, learning, speech, mood and gut mobility.

With regular access to expert nutritional advice for these specific needs extremely difficult to obtain, parents are often forced to undertake this role.? Many parents spend countless hours researching and then preparing meals.? Ratios and portions are constantly monitored and controlled.

It is therefore very disheartening when family and friends make comments like “come on, one won’t hurt” or “are you sure you’re feeding her enough” or “he’s a growing boy, he needs more carbs”.? The diet of most people with PWS doesn’t allow for extras.

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